Parry Romberg syndrome: a close differential diagnosis of linear scleroderma en coup de sabre.

This 45 years old lady complained of asymmetry of her face since the age of 15 years. She also complained of decreased sweating on the left side and an intermittent left hemicranial headache. Examination revealed marked atrophy of the left side of the face involving the skin, subcutaneous tissue and muscles of the orbital, maxillary and mandibular regions. There was no induration or tightening or tethering of the overlying skin. The left half of the tongue was atrophic. Complement levels were normal and ANA was negative.